DOI: https://doi.org/10.14739/2310-1210.2019.2.161515

Клинический случай поздней диагностики системной склеродермии и легочной артериальной гипертензии

L. I. Vasylieva, Ye. D. Yehudina, O. S. Kalashnykova

Аннотация


 

Легочная гипертензия является частым и серьезным осложнением системной склеродермии. Прогноз у пациентов с легочной артериальной гипертензией, ассоциированной со склеродермией, хуже в сравнении с пациентами с идиопатической легочной артериальной гипертензией.

Представили клинический случай поздней диагностики системной склеродермии и ассоциированной с ней легочной артериальной гипертензии. У пациентки 61 года с 20-летним анамнезом синдрома Рейно была впервые диагностирована лимитированная форма системной склеродермии на стадии выраженных проявлений легочной гипертензии со средним давлением в легочной артерии48 ммрт. ст., тяжелой правожелудочковой сердечной недостаточностью и III ФК NYHA. Это подчеркивает необходимость осведомленности и своевременной диагностики лимитированной формы склеродермии и требует повышенного внимания в раннем выявлении легочной гипертензии у таких пациентов.


Ключевые слова


легочная гипертензия; системная склеродермия; катетеризация сердца

Полный текст:

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Литература


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