Clinical case of delayed systemic sclerosis and pulmonary arterial hypertension diagnostics

Authors

  • L. I. Vasylieva SI “Dnepropetrovsk Medical Academy of Health Ministry of Ukraine”, Dnipro,
  • Ye. D. Yehudina SI “Dnepropetrovsk Medical Academy of Health Ministry of Ukraine”, Dnipro,
  • O. S. Kalashnykova SI “Dnepropetrovsk Medical Academy of Health Ministry of Ukraine”, Dnipro,

DOI:

https://doi.org/10.14739/2310-1210.2019.2.161515

Keywords:

pulmonary hypertension, systemic sclerosis, cardiac catheterization

Abstract

 

Pulmonary hypertension is a frequent and severe complication of systemic sclerosis (SSc). SSc-PAH patients have a worse prognosis than patients with idiopathic PAH. We report a case of a patient with delayed SSc and PAH diagnostics. Limited SSc was established in a 61-year-woman with 20 years of Raynaud’s syndrome anamnesis. But diagnosis of SSc-PAH was determined in severe and late symptomatic stage with signs of right heart congestion, NYHA III FC and mPAP 48 mmHg. This emphasizes the need for clinicians to be aware of limited SSc and have a high index of PH suspicion in such patients.

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How to Cite

1.
Vasylieva LI, Yehudina YD, Kalashnykova OS. Clinical case of delayed systemic sclerosis and pulmonary arterial hypertension diagnostics. Zaporozhye Medical Journal [Internet]. 2019Apr.2 [cited 2026May21];21(2). Available from: https://zmj.zsmu.edu.ua/article/view/161515

Issue

Vol. 21 No. 2 (2019)

Section

Case Reports

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